index - Organisation de la cellule musculaire et thérapie de la myopathie centronucléaire autosomique dominante Accéder directement au contenu

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AD-CNM Cavins Myopathie Dullard Endocytosis Cross-bridge kinetics Allele‐specific silencing therapy Allele-specific silencing therapy Myosin Biomarkers Satellite cell Biophysics Dystrophin ACTN2 Developmental myosin heavy chain Migration Dominant centronuclear myopathy Skeletal muscle BAR proteins AAV Cross-presentation Allele specific RNA interference Dynamin 2 Congenital myopathy Diaphragm BMP signaling Duchenne muscular dystrophy DMD Coeur Charcot-Marie-Tooth DMyHC AAV8 Developmental biology BAF Dynamin overexpression Clathrin Amphiphysin AFM Dystrophie musculaire de Duchenne Cell migration Cellules de crête neurale Cell proliferation Autosomal dominant centronuclear myopathy Cytosquelette Disease modifiers Antisense oligonucleotides Ctdnep1 Correlative microscopy Cardiotoxin Duchenne muscular dystrophy A-type lamins Adeno-associated virus vector Muscle DNM2 Mechanotransduction Disease heterogeneity Duchenne Muscular Dystrophy Nuclear envelope Autophagosome Skin Adult patients Caveolae Centronuclear myopathy Cancer Muscular dystrophy Allele-specific silencing Lamin Caveolin Animal models of human disease Core myopathy Clathrine Autophagosome maturation Domaine LEM Gene therapy Adeno-Associated virus Myopathy Adhesion Nucleus Cytoskeleton Neural crest cells CTL Outflow tract Cellular neuroscience Caveolins Dynamine Adeno-associated virus Cavéoles Dynamin Alpha-actinin-2 Nesprin CAV-3 gene Atrial cardiac defects RNA interference Atrial heart defects Actin nucleus Actin Cell signaling Cardiomyopathies Autophagy Dystrophie musculaire d'Emery Dreifuss Becker muscular dystrophy BMD