Relapsing polychondritis: state of the art on clinical practice guidelines. - Université de Lille Accéder directement au contenu
Article Dans Une Revue RMD Open : Rheumatic & Musculoskeletal Diseases Année : 2018

Relapsing polychondritis: state of the art on clinical practice guidelines.

Simona Rednic
  • Fonction : Auteur
Laura Damian
  • Fonction : Auteur
Rosaria Talarico
  • Fonction : Auteur
Alberto Scire Carlo
  • Fonction : Auteur
Tobias Alexander
  • Fonction : Auteur
Alexis Mathian
Lisa Mattews
  • Fonction : Auteur
Cristina Ponte
  • Fonction : Auteur
Paola Toniati
  • Fonction : Auteur
Stefano Bombardieri
  • Fonction : Auteur
Charissa Frank
  • Fonction : Auteur
Matthias Schneider
  • Fonction : Auteur
Vanessa Smith
  • Fonction : Auteur
Maurizio Cutolo
  • Fonction : Auteur
Marta Mosca
  • Fonction : Auteur
Laurent Arnaud
  • Fonction : Auteur


Due to the rarity of relapsing polychondritis (RP), many unmet needs remain in the management of RP. Here, we present a systematic review of clinical practice guidelines (CPGs) published for RP, as well as a list of the most striking unmet needs for this rare disease. We carried out a systematic search in PubMed and Embase based on controlled terms (medical subject headings and Emtree) and keywords of the disease and publication type (CPGs). The systematic literature review identified 20 citations, among which no CPGs could be identified. We identified 11 main areas with unmet needs in the field of RP: the diagnosis strategy for RP; the therapeutic management of RP; the management of pregnancy in RP; the management of the disease in specific age groups (for instance in paediatric-onset RP); the evaluation of adherence to treatment; the follow-up of patients with RP, including the frequency of screening for the potential complications and the optimal imaging tools for each involved region; perioperative and anaesthetic management (due to tracheal involvement); risk of neoplasms in RP, including haematological malignancies; the prevention and management of infections; tools for assessment of disease activity and damage; and patient-reported outcomes and quality of life indicators. Patients and physicians should work together within the frame of the ReCONNET network to derive valuable evidence for obtaining literature-informed CPGs.
Fichier principal
Vignette du fichier
e000788.full.pdf (731.32 Ko) Télécharger le fichier
Origine Fichiers éditeurs autorisés sur une archive ouverte

Dates et versions

hal-04432115 , version 1 (01-02-2024)




Simona Rednic, Laura Damian, Rosaria Talarico, Alberto Scire Carlo, Tobias Alexander, et al.. Relapsing polychondritis: state of the art on clinical practice guidelines.. RMD Open : Rheumatic & Musculoskeletal Diseases, 2018, RMD Open : Rheumatic & Musculoskeletal Diseases, 4, pp.e000788. ⟨10.1136/rmdopen-2018-000788⟩. ⟨hal-04432115⟩
6 Consultations
6 Téléchargements



Gmail Mastodon Facebook X LinkedIn More